Relationship between bronchiectasis and cystic fibrosis

Wonder what kind of CF test involved numbers? Was that a skin test? Usually the genetic test is the only way to know for sure. If you are positive then the new drug that people with CF take has made a HUGE difference for them. If only Non Cystic Fibrosis Bronchiectasis had something like it! I have also read that new genetic variants are being discovered all the time for CF.

@ckscoville @sueinmn
Thanks for the response @ckscoville
It is a very expensive medication. I wonder though if the same mechanism in the drug that allows it to be called a regulator, allowing mucus to be expelled naturally, could be helpful for those where mucus clearance is challenging.

I use postural drainage a lot. If I’m ever in a position where I can’t do this in the future, I think I’d be more prone to infection and a decline in health. Many of us would be.

I suppose there aren’t enough of us to warrant the cost of a new drug that could help with mucus clearance rather than having to position oneself and huff cough with such force. How do people do that with broken ribs? That said, the numbers of BE patients being diagnosed around the world is increasing.

Would there not be other people in circumstances or with illnesses who would benefit though from a targeted medication in addition to Bronchiectasis patients?

I’m still wondering if this particular medication might work even on a short term basis to prevent mucus build up, infection and progression of disease for BE patients, especially if circumstances prevent regular airway clearance. Thanks.

I wonder if one of the BE specialists might have an answer.