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Enlarged aortic root with a family history

Aortic Aneurysms | Last Active: Jan 2 4:45pm | Replies (19)

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@moonboy

I just want to add this: Knowing that you have an enlarged aorta means you can proactively do somethings to prevent it from either getting larger or dissecting entirely. An aortic dissection is an unpredictable, high-stakes medical event. Recognizing symptoms (sudden severe chest or back pain, difficulty breathing, fainting, or symptoms of stroke) and getting to a hospital immediately is critical. With timely intervention, many people can survive and manage their condition successfully.

Here is a refresher of the Ritter Rules for all of us:

URGENCY: Thoracic aortic dissection is a medical emergency. The death rate increases 1%
every hour the diagnosis and surgical repair are delayed.
PAIN: Severe pain is the #1 symptom. Seek immediate emergency medical care for a
sudden onset of severe pain in the chest, stomach, back or neck. The pain is likely to be
sharp, tearing, ripping, moving or so unlike any pain you have ever had that you feel
something is very wrong.
MISDIAGNOSIS: Aortic dissection can mimic heart attack. Heart attacks are far more
common than aortic dissection. But if a heart attack or other important diagnosis is not
clearly and quickly established, then aortic dissection should be quickly considered and
ruled out, particularly if a patient has a family history or features of a genetic syndrome
that predisposes the patient to an aortic aneurysm or dissection.
IMAGING: Get the right scan to rule out aortic dissection. Only three types of imaging studies
can identify aortic aneurysms and dissections: CT, MRI and transesophageal
echocardiogram. A chest X-ray or EKG cannot rule out aortic dissection.
RISK FACTOR: Aortic dissections are often preceded by an enlargement of the first part of
the aorta where it comes out of the heart, called an aortic aneurysm. If you have an
aneurysm, you are at increased risk for an aortic dissection.
RISK FACTOR: A personal or family history of thoracic disease puts you at risk. If you or a
family member is living with an aneurysm or if you have a family member who has had an
aortic dissection, you are at an increased risk for thoracic aortic dissection. You and your
other family members should be evaluated to determine if a predisposition for aortic
aneurysm and dissection is running in the family.
RISK FACTOR: Certain genetic syndromes put you at risk. These genetic syndromes greatly
increase your risk for thoracic aortic disease and a potentially fatal aortic dissection: Marfan
syndrome, Loeys-Dietz syndrome, Turner syndrome and Vascular Ehlers-Danlos syndrome.
RISK FACTOR: Bicuspid aortic valve disease puts you at risk. If you have a bicuspid aortic
valve (two leaflets instead of the typical three), or have had a bicuspid aortic valve replaced,
you need to be monitored for thoracic aortic disease.
TRIGGERS: Lifestyle and trauma can trigger aortic dissection. It is possible to trigger an aortic
dissection through injury to the chest, extreme straining associated with body building, illicit
drug use, poorly controlled high blood pressure or by discontinuing necessary blood
pressure medications. Rarely, pregnancy can trigger an aortic dissection. However, women
with aortic aneurysms and connective tissue disorders who are pregnant are at higher risk
of aortic dissection during late pregnancy and delivery and should be carefully monitored by
a cardiovascular specialist.
PREVENTION: Medical management is essential to preventing aortic dissection. If you have
thoracic aortic disease, medical management that includes optimal blood pressure control,
aortic imaging and genetic counseling is strongly recommended. Talk with your provider.

Credit: JohnRitterFoundation.org

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Replies to "I just want to add this: Knowing that you have an enlarged aorta means you can..."

Thank you, for responding, and for the information! I have a lot to think about.
I made an appointment w this new cardiologist because I knew I had a small dilation and I was concerned about the meds I was prescribed.
My primary doctor prescribed stimulants because I was struggling w pretty severe fatigue. Every time I saw him and expressed distress over the fatigue, he would grill me about the stimulant. He chastised me several times, but I just didn't feel comfortable taking them, (although, they did help.)
When I shared this w my new cardiologist, he didn't comment one way or the other.
Maybe he will after he considers all of my results.
I'm currently wearing a 2 week Holter monitor.
I have an appointment scheduled w him for next December. I hope he gives me guidance sooner than that.

Again, thank you, so much!
I'm glad you are doing so well, and are willing to share.
I'm going to double back and see if you mentioned having your valve replaced when you had the dissection...